Asian Journal of Neurosurgery

CASE REPORT
Year
: 2020  |  Volume : 15  |  Issue : 1  |  Page : 225--229

ATRT of lateral ventricle in a child: A rare tumor at a very rare location


Fayçal Lakhdar1, Mohammed Benzagmout1, Yasser Arkha2, Khalid Chakour1, Mohammed El Faiz Chaoui1 
1 Department of Neurosurgery, Hassan II Hospital, University Sidi Mohammed Ben Abdellah, Fez, Morocco
2 Department of Neurosurgery, Hopital des Spéciaités, University Mohammed V of Medecine, Rabat, Morocco

Correspondence Address:
Prof. Fayçal Lakhdar
10, Rue Oulad Jerrar Souissi, Rabat, BP 10100
Morocco

Atypical teratoid/rhabdoid tumors (AT/RTs) of infancy are highly malignant central nervous system neoplasms that are most commonly seen during the first 2 years of life with limited therapeutic options. To date, only two cases have been described in the lateral ventricle. A 4-year-old boy presented with a 4-month history of increased intracranial pressure. Cerebral magnetic resonance imaging (MRI) revealed a huge intraventricular tumor, occupying the entire temporal horn and the body of the left lateral ventricle. The boy was operated through a left temporal transventricular approach with gross total removal of the lesion. The histopathological diagnosis was an AT/RT. The infant underwent adjuvant chemotherapy and radiation therapy. The 1-year MRI of control showed a local recurrence of the tumor. Then after, Gamma Knife radiosurgery was performed because of the small volume and the deep location of the lesion. At the 3-month follow-up, the MRI showed a significant growth of the tumor volume, and the child was given additional adjuvant chemotherapy. Unfortunately, he died 9 months later. AT/RT of the lateral ventricle is a very rare tumor in children, associated with a poor prognosis in spite of multimodal treatment. Gamma knife surgery (GKS) was rarely reported as a treatment modality of AT/RT. The aim of this work is to discuss about the rarity of this tumor and the best treatment strategy to improve prognosis.


How to cite this article:
Lakhdar F, Benzagmout M, Arkha Y, Chakour K, Chaoui ME. ATRT of lateral ventricle in a child: A rare tumor at a very rare location.Asian J Neurosurg 2020;15:225-229


How to cite this URL:
Lakhdar F, Benzagmout M, Arkha Y, Chakour K, Chaoui ME. ATRT of lateral ventricle in a child: A rare tumor at a very rare location. Asian J Neurosurg [serial online] 2020 [cited 2020 Aug 7 ];15:225-229
Available from: http://www.asianjns.org/article.asp?issn=1793-5482;year=2020;volume=15;issue=1;spage=225;epage=229;aulast=Lakhdar;type=0